Cutis laxa (elastolysis) in a patient with Sjögren’s syndrome

Cutis laxa (elastolysis) in a patient with Sjögren's syndrome.

Cutis laxa (CL), or elastolysis, is a rare inherited or acquired connective tissue disorder where the skin becomes inelastic and hangs loosely in folds. Sjögren’s syndrome (SS) is a chronic inflammatory disease characterized by diminished lacrimal and salivary gland function. SS may be a primary disease and may accompany other rheumatologic diseases. To our knowledge, the simultaneous occurrenc...

Sotos syndrome and cutis laxa.

Characteristics suggestive of connective tissue dysfunction have been described in Sotos syndrome and include joint hyperextensibility, pes planus, and a high arched palate. A variety of cutis laxa syndromes have also been described, some of them exhibiting mental retardation, but no reports have drawn an association with overgrowth or abnormal facies characteristic of Sotos syndrome. We report...

Cutis laxa: a feature of Costello syndrome.

Cutis Laxa syndrome: a case report

Cutis laxa (CL) is a heterogeneous group of inherited and acquired connective tissue disorders characterized by a loose skin and variable systemic involvement (inguinal hernia, cardiopulmonary disease, and emphysema). Autosomal dominant, autosomal recessive and x-linked recessive patterns have been described in the inherited forms. Acquired forms of this disease have been associated with a prev...

Cutis laxa and the Costello syndrome.